Sonographic diagnosis of Obstructed Hemivagina and Ipsilateral Renal Anomaly Syndrome: a report of two cases
نویسندگان
چکیده
Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome is a rare urogenital anomaly. Patients typically present at puberty, shortly after menarche with increasing pelvic pain, dysmenorrhea and pelvic mass. There may be a known history of unilateral renal agenesis. Diagnosis can usually be established by ultrasound or magnetic resonance imaging. Resection of the vaginal septum is the treatment of choice. Early diagnosis and treatment can relieve symptoms, prevent complications and preserve fertility. We present two cases of OHVIRA syndrome diagnosed by ultrasound to promote recognition of this rare but important condition.
منابع مشابه
Herlyn-Werner-Wunderlich Syndrome: Sonographic and Magnetic Resonance (MR) Imaging Findings of This Rare Urogenital Anomaly
BACKGROUND Herlyn-Werner-Wunderlich syndrome is a rare congenital urogenital anomaly characterised by uterus didelphys with blind hemivagina and ipsilateral renal agenesis. Children usually have progressive pelvic pain after menarche, palpable mass due to hemihaemato(metro)colpos or pelvic inflammatory disease. The diagnosis usually requires a suspicion of this rare genitourinary syndrome. CA...
متن کاملA case of obstructed hemivagina and ipsilateral renal anomaly syndrome (OHVIRA) with a single uterus, unrecognized before labor and followed by an intrapartal rupture of obstructed hemivagina
Objective Müllerian duct anomalies are congenital anomalies of the female genital tract resulting from non-development or non-fusion of the Müllerian ducts, or failed resorption of the uterine septum. The acronym for obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) was created to describe patients with an obstructed hemivagina and ipsilateral renal anomaly and enables inclusion of o...
متن کاملگزارش یک مورد ناهنجاری تکاملی یکطرفه مجرای مولر
Developmental defect of Mullerian duct is a congenital malformation characterized by anomalies in famale upper genital organs. As the anomaly is associated with obstruction of the duct, other congenital anomalies of urinary tract specially ipsilateral ranal agenesis are common. This anomaly is often discovered in adolescent period and is usually asymptomatic until puberty. To discover this anom...
متن کاملUterine didelphys associated with obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome
Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome is a rare complex of structural abnormalities of the female urogenital tract. A 17-year-old girl with uterine didelphys associated with OHVIRA syndrome presented with progressive development of cyclic lower abdominal discomfort and a large abdominopelvic mass. We describe the findings from ultrasound, computed tomography (CT)...
متن کاملClinical Implications of Obstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA) Syndrome in the Prepubertal Age Group
PURPOSE Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome is a rare syndrome characterized by Müllerian duct and renal anomalies. It is usually regarded as a disease of adolescence; however, due to a number of possible problems, the management of patients before puberty should not be overlooked. We assessed the clinical course of prepubertal patients to propose appropriate m...
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